Resumo

PEREIRA, Edmundo Luís Rodrigues; MENDES, Thaís Sousa  e  SOUSA, Erica Aranha de. Neurofibroma of brachial plexus: case report. Rev. Para. Med. [online]. 2006, vol.20, n.3, pp.59-63. ISSN 0101-5907.

Neurofibromatosis is an dominant autosomic disease with skin abnormalities and nervous system neoplasms - Café-au-lait spots and fibrous peripheral neoplasms (neurofibromas) are the main features. There is also a high incidence of central nervous system, cranial nerves and spinal cord primary neoplasms, with tendency to malignization. OBJECTIVE: A six years-old female patient with type 1 neurofibromatosis, harboring a huge right braquial plexus neurofibroma. METHODS: Description and analysis of main clinical-pathological features of a young female harboring a huge mass in the brachial plexus treated at the Santa Casa Hospital. CASE REPORT: Patient J.L.A., female, six years-old, with complaints of pain and a tumor in the right axilar region, with extension to right median and cubital nerves. MR examination revealed a large mass at the brachial plexus. A microsurgery was performed in a two-staged fashion, with complete removal of lesion. Histology revealed a typic neurofibroma, with no signs of malignancy. CONCLUSIONS: Malignancy of a neurofibroma is always a concerning. Thus, early interventions and complete removal of such lesions are the goal of the treatment.

Palavras-chave : neurofibromatosis; brachial plexus tumor; phakomatoses; microsurgery.

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